Hepatic fibrosis

a rare hereditary disorder characterized by periportal fibrosis with irregularly shaped proliferating bile ducts, intrahepatic portal hypertension, and esophageal varices

Description
Hepatic fibrosis can be congenital(CHF) or acquired (see fibrosis). CHF is associated with an impairment of renal function, usually caused by an autosomal recessive polycystic kidney disease, which is a severe form of polycystic kidney disease. The hepatic manifestations of CHF were first described in 1856. In 1961, the term CHF, with its varied clinical manifestations, was recognized. CHF is inherited in an autosomal recessive fashion, but sporadic cases do occur.